Manifestación orbitaria de la enfermedad de Wegener
- JC Pinto Bonilla
- A Lanuza García
- E Hernández Galilea
- G Günes
- MC Arias López
ISSN: 0365-6691
Datum der Publikation: 2004
Ausgabe: 79
Nummer: 5
Seiten: 243-246
Art: Artikel
Andere Publikationen in: Archivos de la Sociedad Española de Oftalmologia
Zusammenfassung
Case report: Patient who consults for a recidivant orbital mass. Preliminary clinical and image studies suggested an initial differential diagnosis between a lachrymal gland tumor or an orbital located pseudotumor. However, the clinical evolution of the case required a re-evaluation of the preliminary diagnosis. The clinical, histologic and serologic findings were key in the final diagnosis. Discussion: Wegener´s granulomatosis is a necrotizing vasculitis. Classically it affects the upper airways, lungs and kidneys. Between 30% and 70% of patients present ophthalmic symptoms during the course of the illness. Ophthalmic affectation prior to systemic manifestations is less frequent and could delay final diagnosis.
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