Linfangiectasia intestinal primaria como causa de hipoalbuminemia

  1. A. Hortal Benito Sendín 1
  2. María Carla Criado Muriel 1
  3. R. Torres Peral 1
  4. E. García Serrano 1
  5. N. Álvarez Álvarez 1
  1. 1 Hospital Universitario de Salamanca
    info

    Hospital Universitario de Salamanca

    Salamanca, España

    ROR https://ror.org/0131vfw26

Journal:
Acta pediátrica española

ISSN: 0001-6640

Year of publication: 2014

Volume: 72

Issue: 11

Pages: 393-399

Type: Article

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Abstract

Primary intestinal lymphangiectasia is a congenital malformation of the subserosal lymph vessels associated to a protein-losing enteropathy. The obstruction of the lymphatic drainage of the intestine leads to a rupture of the intestinal lymph vessels in which the lymph spreads to the intestinal lumen, which causes hypoproteinemia-related edemas, hypogammaglobulinemia-related immunodeficiency, lymphocytopenia and steatorrhea. We present a clinical case of a lactating 6-months old infant with severe infections, hypoalbuminemia, edemas and steatorrhea in which an intestinal biopsy confirmed the diagnosis of intestinal lymphangiectasia and a triggering cause was ruled out with other complementary tests.

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